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Measurement Reliability and Functional Validity of Bruch's Membrane Calcification in Pseudoxanthoma Elasticum: PROPXE Study Report 2.
Giger Jason A W, Ansari Georg, Terry Sharon F, Charbel Issa Peter, Pfau Kristina, Pfau Maximilian
Invest Ophthalmol Vis SciNov 20250 citationsObservational Study
This study found reliable measurement of Bruch's membrane calcification in PXE, which increases with age and strongly correlates with delayed rod-mediated dark adaptation, making it a potential early severity marker for treatment.